Caroli disease

Caroli disease


Caroli disease is a rare inherited disorder characterized by cystic dilatation (or ectasia) of the bile ducts within the liver.


Patients experience episodes of cholestasis and abdominal pain as well as development of stones within the bile ducts.


Underlying cause of Caroli disease is poorly understood and believed to be of genetic nature.


Around 1:100’000

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Last Updated on 17 May 2021